Combined Tc-99m MDP and Tc-99m labeled RBC imaging in a case of Maffucci's syndrome
Clinical Nuclear Medicine, cilt.29, sa.12, ss.817-820, 2004 (SCI-Expanded, Scopus)
- Yayın Türü: Makale / Tam Makale
- Cilt numarası: 29 Sayı: 12
- Basım Tarihi: 2004
- Doi Numarası: 10.1097/00003072-200412000-00015
- Dergi Adı: Clinical Nuclear Medicine
- Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
- Sayfa Sayıları: ss.817-820
- Anahtar Kelimeler: Maffucci's syndrome, Scintigraphy, Tc-99m
- Maltepe Üniversitesi Adresli: Hayır
Özet
Maffucci's syndrome is characterized by multiple en chondromas combined with hemangiomas and less commonly lymphangiomas. The extent of skeletal involvement is variable in this rare nonhereditary syndrome, but the most frequent sites of enchondromas are the metacarpals and the phalanges of the hands and less commonly the feet. The bony and soft tissue lesions are likely to be much more extensive on one side of the body than the other. The clinical problems are progressive shortening of the involved extremity, angular deformity, pathologic fracture, and malignant transformation of the skeletal lesions. Effects of the disease range from those requiring minor adjustments in activities of daily life to almost total incapacitation. We report a case of 20-year-old man with Maffucci's syndrome involving the right lower and upper distal extremities with a variety of vascular proliferations.